副肿瘤性天疱疮并发盆腔内Castleman病

发布时间：2018-07-04 08:14

本文选题：副肿瘤性天疱疮 + 巨淋巴结增生　；参考：《临床皮肤科杂志》2017年03期

【摘要】：报告1例副肿瘤天疱疮并发儿童型Castleman病。患者男,15岁。黏膜糜烂5个月余,全身红斑、水疱伴发热4个月。皮肤科检查:全身皮肤泛发红斑、斑丘疹,大小不一的厚壁水疱,不易破溃,尼氏征阴性。黏膜糜烂、溃疡,表面附着脓性分泌物。皮损组织病理及间接免疫荧光支持副肿瘤性天疱疮诊断,盆腔CT提示左侧髂外动脉、闭孔旁单发结节和肿物,切除肿物经组织病理证实为Castleman病。术后15 d患者死于感染性休克。
[Abstract]:A case of paraneoplastic pemphigus complicated with childhood Castleman disease was reported. The patient was 15 years old. Mucosal erosion more than 5 months, systemic erythema, blister with fever for 4 months. Dermatology examination: systemic skin erythema, macular papules, different sizes of thick blisters, not easy to break, Nissl sign negative. Mucosal erosion, ulcer, surface attachment purulent secretion. The diagnosis of paraneoplastic pemphigus was supported by histopathology and indirect immunofluorescence. Pelvic CT revealed left external iliac artery, solitary nodules and masses adjacent to obturator, and Castleman's disease was confirmed by histopathology. The patients died of septic shock 15 days after operation.
【作者单位】：中国中医科学院广安门医院皮肤科;
【分类号】：R73;R758.66

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