左冠状动脉异常起源于肺动脉综合征CTCA表现的分折

发布时间：2018-07-04 06:51

本文选题：冠状动脉异常起源 + 多层螺旋CT　；参考：《中山大学学报(医学科学版)》2015年01期

【摘要】：【目的】分析左冠状动脉异常起源于肺动脉(ALCAPA)综合征的多排螺旋CT冠状动脉成像(MDCTCA)表现并复习文献,以期提高对该综合征的认识。【方法】对3例经手术证实的ALCAPA综合征患者的CTCA表现和临床资料进行回顾性分析。3例患者均于术前行CTCA检查,其中2例于术后各复查1次CTCA。【结果】3例患者术前CTCA检查均可清晰显示左冠状动脉起源于肺动脉,与术中所见相符;其中2例患儿出生后不久开始出现心功能不全症状,CTCA示双侧冠状动脉未见扩张,左心室增大,符合"婴儿型";1例患儿婴儿期无症状,CTCA可见右侧冠状动脉主干及分支扩张迂曲,左、右冠状动脉间见多条侧枝血管吻合,符合"成人型";1例患者合并动脉导管未闭及永存左上腔静脉,1例合并左肾重复畸形。【结论】CTCA技术是ALCAPA综合征诊断、分型及术后随访的重要手段。
[Abstract]:[objective] to analyze the findings of multi-slice spiral CT coronary angiography (MDCTCA) with anomalous origin of left coronary artery from pulmonary artery syndrome (ALCAPA) and to review the literature. [methods] CTCA findings and clinical data of 3 patients with ALCAPA syndrome proved by surgery were retrospectively analyzed. In 2 cases, CTCA was performed once after operation. [results] preoperative CTCA examination in 3 cases showed clearly that the left coronary artery originated from the pulmonary artery, which was consistent with the intraoperative findings. In 2 cases, cardiac insufficiency began to appear shortly after birth. CTCA showed no dilation of bilateral coronary artery and enlargement of left ventricle. In accordance with "infantile type", 1 case of infantile asymptomatic CTCA showed right coronary artery trunk and branch dilatation and detour. Multiple collateral anastomoses were found between left and right coronary arteries, which were consistent with the diagnosis of ALCAPA syndrome in 1 case of "adult type" with patent ductus arteriosus and 1 case of persistent left superior vena cava with duplication of left kidney. [conclusion] CTCA technique is the diagnosis of ALCAPA syndrome. Classification and postoperative follow-up of the important means.
【作者单位】：中山大学附属第一医院放射科;
【分类号】：R816.92;R725.4

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