婴儿及少儿型常染色体隐性多囊性肾病的CT与MRI表现

发布时间：2018-04-05 08:32

  本文选题：常染色体隐性多囊性肾病　切入点：磁共振成像　出处：《中国医学影像技术》2017年02期

【摘要】：目的观察婴儿及少儿型常染色体隐性多囊性肾病(ARPKD)的CT、MRI表现。方法回顾性分析11例婴儿及少儿型ARPKD患者腹部CT及MRI上肝叶比例、双肾体积改变以及胆管与肾脏囊样病灶的表现。结果 11例婴儿及少儿型ARPKD患者中,5例(5/11,45.45%)肝叶比例失调。5例(5/11,45.45%)中央区域肝内胆管以梭形扩张为主、3例(3/11,27.27%)肝边缘部胆管扩张明显、3例(3/11,27.27%)沿门静脉周围可见多发囊样灶。2例(2/11,18.18%)肾脏体积增大。8例(8/11,72.73%)双肾髓质可见多发小囊样灶、3例(3/11,27.27%)双肾皮髓质多发囊肿。8例(8/11,72.73%)门静脉增粗、脾大。2例(2/11,18.18%)腹部可见多发肿大淋巴结。5例(5/11,45.45%)MR平扫T1WI显示双肾皮髓质分界不清。结论婴儿或少儿型ARPKD以肝胆改变为主,特征性CT及MRI表现为肝叶比例与肾脏体积的改变合并胆管扩张及双肾囊样灶。
[Abstract]:Objective to observe the CT MRI findings of autosomal recessive polycystic nephropathy (ARPKD) in infants and children.Methods the ratio of upper lobe of abdomen CT and MRI, the changes of bilateral renal volume and cystic lesions of bile duct and kidney in 11 cases of infantile and juvenile ARPKD were analyzed retrospectively.缁撴灉 11渚嬪┐鍎垮強灏戝効鍨婣RPKD鎮ｈ，

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