多脾综合征心脏结构特点的超声心动图诊断

发布时间：2018-05-27 12:21

本文选题：多脾综合征 + 先天性心脏病　；参考：《中国超声医学杂志》2015年05期

【摘要】：目的探讨多脾综合征患者合并心脏畸形的特点,为超声诊断及外科治疗提供思路。方法采用超声心动图显示45例多脾综合征患者心脏畸形并分析其特点,回顾分析34例多脾综合征患者外科手术方式特点。结果 45例多脾综合征患者均存在房间隔发育异常;40例(88.9%)合并室问隔发育异常;房室瓣发育异常发生率较高,共25例(55.6%);21例(46.7%)患者存在动脉-心室连接异常;32例(71.1%)患者存在右室流出道及肺动脉发育异常;39例(86.7%)存在体静脉及肺静脉引流异常。34例患者接受外科手术,包括双心室矫治及Fontan类手术。结论多脾综合征多合并复杂心脏畸形,超声心动图可以较准确诊断多脾综合征及其心脏畸形情况,决策外科手术方式。
[Abstract]:Objective to investigate the characteristics of heart malformation in patients with polysplenic syndrome and to provide ideas for ultrasonic diagnosis and surgical treatment. Methods 45 patients with polysplenic syndrome were examined by echocardiography and their characteristics were analyzed. The surgical methods of 34 patients with polysplenic syndrome were analyzed retrospectively. Results Atrial septal dysplasia was found in all 45 patients with polysplenic syndrome (n = 40) accompanied with abnormal development of interventricular septum, and the incidence of abnormal development of atrioventricular valve was higher. There were 32 cases with abnormal arterial-ventricular connection (32 cases with abnormal arterial-ventricular connection) and 39 cases with abnormal development of right ventricular outflow tract and pulmonary artery (39 cases with abnormal development of right ventricular outflow tract and pulmonary artery). 34 cases with abnormal drainage of systemic vein and pulmonary vein were operated on. Including biventricular correction and Fontan type surgery. Conclusion Polysplenic syndrome is complicated with complex cardiac malformation. Echocardiography can accurately diagnose polysplenic syndrome and its cardiac malformation, and make surgical decision.
【作者单位】：中国医学科学院北京阜外心血管病医院超声科;
【分类号】：R540.45;R551.1

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