先天性矫正型大动脉转位的超声心动图特征

发布时间：2018-06-28 17:36

本文选题：超声心动描记术 + 先天性矫正型大动脉转位　；参考：《中国超声医学杂志》2015年10期

【摘要】：目的采用超声心动图对先天性矫正型大动脉转位(ccTGA)的解剖特征进行分析。方法超声心动图检查,且诊断为ccTGA的患儿45例,采用Van Praagh顺序节段分析法进行诊断。结果 (1)心房-心室连接不一致、心室-大动脉连接不一致:{S,L,L}40例(包括左位心30例,孤立性右位心10例);{I,D,D}4例(包括左位心2例,镜像右位心2例);{S,L,D}1例,为左位心。(2)合并房室瓣异常:房室瓣结构畸形7例。(3)其他合并畸形40例(88.9%),其中,最常见的是肺动脉瓣狭窄或肺动脉瓣下狭窄(29例,64.4%)和室间隔缺损(25例,55.6%)。结论 {S,L,L}是ccTGA最常见的病理解剖形式,此外也可以表现为{I,D,D}和{S,L,D};在ccTGA患者中,解剖三尖瓣功能性反流较常见且较严重;肺动脉瓣狭窄或肺动脉瓣下狭窄和室间隔缺损是其最常见的合并畸形。
[Abstract]:Objective to analyze the anatomical features of congenital corrected transposition of great arteries (ccTGA) by echocardiography. Methods 45 children with ccTGA diagnosed by echocardiography were diagnosed by Van Praagh sequential segmental analysis. Results (1) Atrial-ventricular connection was inconsistent and ventricular-great artery connection was inconsistent: 40 cases (including 30 cases of left and 10 cases of isolated right heart), 4 cases (including 2 cases of left and 2 cases of mirror right heart), 1 case of {SLD}, (2) there were 7 cases of atrioventricular valve malformation, (3) 40 cases (88.9%) of other complicated malformations, the most common of which were pulmonary valve stenosis or subvalvular stenosis (29 cases, 64.4%) and ventricular septal defect (25 cases, 55.6%). Conclusion\ {Ssll} is the most common pathological anatomic form of ccTGA, and it can also be characterized by {Ignadou D} and {SnlD}. In ccTGA patients, the anatomic tricuspid functional regurgitation is more common and more serious. Pulmonary stenosis or subvalvular stenosis and ventricular septal defect are the most common associated deformities.
【作者单位】：复旦大学附属儿科医院心血管中心;上海市出生缺陷重点实验室;
【基金】：上海市科委重点实验室专项(No.13dz2260600)
【分类号】：R725.4;R540.45

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