Dyke-Davidoff-Masson综合征CT及MRI特征分析

发布时间：2018-03-15 09:39

  本文选题：Dyke-Davidoff-Masson综合征　切入点：单侧大脑萎缩　出处：《广东医学》2017年S1期 　论文类型：期刊论文

【摘要】：目的探讨Dyke-Davidoff-Masson(DDM)综合征的临床及影像学特征,提高对DDM综合征的认识并减少漏诊及误诊。方法回顾性分析经CT及MRI诊断的5例DDM综合征患者的临床及影像学资料,总结其影像学诊断依据。结果 5例患者中男2例,女3例,发病年龄9~55岁,平均(32±15)岁。临床表现为癫痫发作,面部不对称及对侧肢体无力。影像学均表现为左侧大脑萎缩,患侧侧脑室扩大,中线结构向患侧偏移,患侧颅窝缩小,颅骨增厚。1例合并患侧丘脑、豆状核及大脑脚萎缩,1例合并脑实质软化灶,1例合并脑穿通畸形囊肿。结论 DDM综合征具有典型的影像学表现,结合临床表现可以作出诊断。
[Abstract]:Objective to investigate the clinical and imaging features of Dyke-Davidoff-Masson DDM syndrome, to improve the understanding of DDM syndrome and to reduce misdiagnosis and misdiagnosis. Methods the clinical and imaging data of 5 patients with DDM syndrome diagnosed by CT and MRI were analyzed retrospectively. Results among the 5 patients, 2 were male and 3 were female. The onset age was 9 to 55 years (mean 32 卤15) years. The clinical manifestations were epileptic seizures, facial asymmetry and contralateral limb weakness. The ventriculus of the affected side was enlarged, the midline structure shifted to the affected side, the cranial fossa was reduced, and the skull was thickened in 1 cases with the thalamus of the affected side. Lentiform nucleus and atrophy of the cerebral feet were found in 1 case with cerebral parenchymatomalacia and 1 case with cerebral perforation malformation cyst. Conclusion DDM syndrome has typical imaging features and can be diagnosed with clinical manifestations.
【作者单位】： 中山市东升医院影像科;
【分类号】：R445.2;R742;R816.1
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