儿童木村病合并肾病综合征3例分析并文献复习

发布时间：2018-03-20 23:24

本文选题：木村病　切入点：肾病综合征　出处：《中国实用儿科杂志》2017年08期 　论文类型：期刊论文

【摘要】：目的提高对儿童木村病合并肾病综合征的诊断及治疗水平。方法对西安市儿童医院肾内科2011—2015年所诊断的3例木村病合并肾病综合征进行病例回顾,同时查找相关国内外文献资料,以了解目前儿童木村病的发病机制、诊断及治疗方案。结果木村病是一种罕见的以淋巴结、软组织及唾液腺损害为主的慢性免疫炎性疾病,多见于28~32岁的亚洲人群,好发于男性。目前对此病的病因及其发病机制尚不清楚。组织病理是诊断木村病的惟一手段,肾活检作为肾脏疾病诊断的金标准,对于诊断及治疗木村病肾损害有很大帮助。目前的治疗主要依赖药物治疗,一般都需要用激素联合免疫抑制剂。结论木村病属慢性起病,呈良性病程,但易复发,一般无恶变倾向。
[Abstract]:Objective to improve the diagnosis and treatment of children's Kimura disease complicated with nephrotic syndrome. Methods three cases of wooden village disease complicated with nephrotic syndrome diagnosed in Department of Renal Medicine of Xi'an Children's Hospital from 2011 to 2015 were reviewed. In order to find out the pathogenesis, diagnosis and treatment of the disease in children, Musun disease is a rare chronic immune inflammatory disease with lymph node, soft tissue and salivary gland lesion. It is more common in the Asian population of 28 to 32 years old, and is more common in men. At present, it is not clear about the etiology and pathogenesis of the disease. Histopathology is the only means of diagnosis of Kimura disease, and renal biopsy is the golden standard for the diagnosis of renal diseases. It is of great help to diagnose and treat the renal damage caused by Kimura disease. At present, the treatment mainly depends on drug therapy, and it usually needs hormone combined with immunosuppressant. Conclusion Kimura disease is a chronic disease with benign course of disease, but it is easy to recur. There is generally no tendency to change.
【作者单位】：西北妇女儿童医院肾内科;西安市儿童医院肾内科;
【分类号】：R725.9;R726.9

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