罕见小儿眼牵牛花综合征超声表现及特征

发布时间：2018-06-20 19:19

本文选题：牵牛花综合征 + 小儿　；参考：《四川大学学报(医学版)》2017年04期

【摘要】：目的探讨小儿牵牛花综合征(morning glory syndrome,MGS)患眼超声表现及特点。方法将2005~2016年确诊为MGS并有完整高频超声眼部检查资料的6例患儿(7只患眼)纳入研究,回顾性分析其超声及临床表现。结果 6例患儿(男4例,女2例)诊断时年龄5~60月,中位年龄8.5月。12只眼中7只MGS,伴视网膜脱离2例;伴永存原始玻璃体增生症(PHPV)及眼小1例,对侧眼白内障;仅伴PHPV 1例;双眼MGS 1例;无合并眼病MGS 1例。二维超声表现:7只MGS患眼视盘区呈局限性凹陷状,边界清楚,形态规则,与玻璃体相通,深面突向眼球后极视神经走行方向,病灶最大深度为4~15mm,平均(8.29±4.42)mm,最大宽度为4~11mm,平均(6.86±2.67)mm;凹陷内未见正常视神经回声;局部放大观察5个凹陷病灶底部显示有弱回声充填;7只患眼视神经轴末端与凹陷底部相距距离不一,最近者呈紧贴状态,最远者相距约4.5mm。彩色血流显像:7例凹陷区周边血流信号(Adler,2~3级)明显较凹陷内部血流(Adler,0~1级)丰富。结论 MGS眼常伴其他眼部病变。视盘区局限性凹陷区为该病典型超声表现特征。超声有助诊断MGS,且还能进一步发现其他伴发眼病。
[Abstract]:Objective to investigate the ultrasonographic features of morning glory syndrome in children with morning glory syndrome. Methods from 2005 to 2016, 7 eyes of 6 children with MGS diagnosed as MGS were included in the study, and their ultrasound and clinical manifestations were analyzed retrospectively. Results 6 cases (male 4 cases, female 2 cases) were diagnosed at the age of 5 ~ 60 months, median age was 8.5 months, 7 MGSs with retinal detachment (2 cases), 1 case with persistent primary vitreous hyperplasia (PHPVV), 1 case with small eye, 1 case with cataract of contralateral eye, 1 case with PHPV. One case had bilateral MGS and 1 case had no MGS complicated with ophthalmopathy. Two-dimensional ultrasound showed that the optic disc area of 7 MGS eyes was concave, with clear boundary, regular shape, communicating with the vitreous body, and the deep face protruding to the posterior pole of the eyeball optic nerve. The maximum depth of the lesion was 4 ~ 15mm, the mean depth was 8.29 卤4.42mm, the maximum width was 411mm, and the average width was 6.86 卤2.67mm. there was no normal optic nerve echo in the sag, and the local magnification observation showed that there was weak echo filling at the bottom of the lesion, and the distance between the axial end of the optic nerve and the bottom of the concave was different. The closest was in a close position, and the farthest was about 4.5 mm. Color blood flow imaging showed that the peripheral blood flow signals of 7 cases were significantly more abundant than that of adlerian grade 1). Conclusion MGS eyes are often accompanied with other ocular lesions. The localized concave area of the optic disc is the typical ultrasonographic feature of the disease. Ultrasound is helpful in the diagnosis of MGSand can further detect other ocular diseases.
【作者单位】：四川大学华西医院超声科;
【分类号】：R445.1;R774.6

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