Berry综合征的超声及CT表现

发布时间：2018-11-25 10:20

【摘要】：目的:探讨Berry综合征的CT及超声表现及其诊断价值。方法:回顾性分析6例(男2例,女4例,年龄18天~7.5个月,平均81.2天)Berry综合征的超声和CT图像,所有患者均经手术病理证实。患者均行超声心动图检查,其中3例行CT增强检查。结果:6例中3例经超声、3例经CT增强诊断为Berry综合征,本组Berry综合征的主要影像表现包括远侧主-肺动脉间隔缺损6例。右肺动脉部分或完全异常起源于升主动脉(2例表现为右肺动脉开口骑跨于远侧间隔缺损上,4例右肺动脉完全开口于升主动脉)。主动脉弓离断(其中A型4例,B型1例)或狭窄(1例)伴室间隔完整;4例可见粗大的动脉导管,2例动脉导管细小伴侧支动脉扩张。合并畸形以房间隔缺损最为常见(共5例),左侧冠脉起源于窦管交界处2例。结论:Berry综合征的影像学具有各种组合畸形,CT及超声能够诊断Berry综合征的各种异常改变,超声是术前诊断的首选方法,CT检查是有益的补充检查手段。
[Abstract]:Objective: to investigate the CT and ultrasound findings of Berry syndrome and their diagnostic value. Methods: the ultrasound and CT images of 6 patients with Berry syndrome (male 2, female 4; age 18 days to 7.5 months, mean 81.2 days) were retrospectively analyzed. All the patients were confirmed by operation and pathology. Echocardiography was performed in all patients, 3 of whom underwent CT enhancement. Results: of the 6 cases, 3 cases were diagnosed as Berry syndrome by ultrasound and 3 cases by CT enhancement. The main imaging manifestations of Berry syndrome included 6 cases of distal aortopulmonary septal defect. The partial or complete abnormality of the right pulmonary artery originated from the ascending aorta (2 cases with the right pulmonary artery opening straddling the distal septal defect and 4 cases with the right pulmonary artery completely opening the ascending aorta). The aortic arch was cut off (4 cases of type A, 1 case of type B) or stenosis (1 case) accompanied with complete ventricular septum, 4 cases were large ductus arteriosus, 2 cases were dilatation of small artery with collateral artery. Atrial septal defect was the most common deformity (5 cases), and left coronary artery originated from the junction of sinus canal in 2 cases. Conclusion: the imaging features of Berry syndrome have various combination deformities. CT and ultrasound can diagnose various abnormal changes of Berry syndrome. Ultrasound is the first choice in preoperative diagnosis, and CT is a useful supplementary examination method.
【作者单位】：首都医科大学附属北京儿童医院影像中心;
【基金】：首都临床特色应用研究基金资助(Z141107002514005)
【分类号】：R445.1;R541.1

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