纤维肉瘤样隆突性皮肤纤维肉瘤诊治研究进展

发布时间：2018-04-28 15:13

本文选题：隆突性皮肤纤维肉瘤 + 纤维肉瘤样　；参考：《临床皮肤科杂志》2014年04期

【摘要】：纤维肉瘤样隆突性皮肤纤维肉瘤(fibrosarcomatous dermatofibrosarcoma protuberans,FS-DFSP)是一种罕见而独特的隆突性皮肤纤维肉瘤(dermatofibrosarcoma protuberans,DFSP)亚型。有别于经典DFSP交界恶性/潜在低度恶性的生物学行为,FS-DFSP具有较高的复发率及转移率,因此目前认为其生物学行为属明确恶性。由于小面积纤维肉瘤样变区域即具有极为重要的临床意义,因此临床应重视FS-DFSP的诊断,及时行组织病理检查。尽管美国国家综合癌症网络(National Comprehensive Cancer Network,NCCN)公布了DFSP的临床实践指南,但目前对于FS-DFSP患者还没有公认的或特别推荐的治疗选择,FSDFSP的诊治尚存在一些问题。加深对FS-DFSP的理解和认识有助于指导临床诊断和鉴别诊断、治疗选择及预后判断。
[Abstract]:Fibrosarcoma like fibrosarcomatous dermatofibrosarcoma protuberans (FS-DFSP) is a rare and unique protuberant cutaneous fibrosarcoma (dermatofibrosarcoma protuberans, DFSP) subtype. It is different from the classical DFSP junction malignant / potentially low malignant biological behavior, and FS-DFSP has a high recurrence rate. It is believed that the biological behavior is clearly malignant. Because the small area fibrosarcoma like area is of great significance, we should pay attention to the diagnosis of FS-DFSP and make the histopathological examination in time. Although the national integrated cancer network (National Comprehensive Cancer Network, NCCN) has published the DFS P's clinical practice guide, however, has not yet been recognized or specially recommended for FS-DFSP patients. There are still some problems in the diagnosis and treatment of FSDFSP. To deepen the understanding and understanding of FS-DFSP helps to guide the clinical diagnosis and differential diagnosis, treatment selection and prognosis.

【作者单位】：中国人民解放军南京军区南京总医院病理科;
【基金】：中国博士后科学基金(201150M1575)面上资助项目;中国博士后科学基金(2012T50895)特别资助项目
【分类号】：R739.5

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