多脾综合征的CT诊断

发布时间：2018-06-23 17:54

本文选题：多脾综合征 + 内脏　；参考：《临床放射学杂志》2015年12期

【摘要】：目的探讨多脾综合征的MSCT表现及其诊断价值。方法回顾性分析10例多脾综合征患者的临床和CT表现。结果 9例合并多器官及心血管系统畸形,1例仅合并房间隔缺损。CT表现主要有:(1)多个脾结节。脾脏数目4~14个;(2)内脏异常。全内脏反位1例,部分内脏反位3例,短胰6例,环状胰腺1例,水平肝2例,小肠旋转不良1例,马蹄肾1例,双肺左侧异构3例;(3)心血管畸形。下腔静脉肝段缺如,肝静脉直接汇入右心房,奇静脉或半奇静脉扩张与上腔静脉异常连接8例;双上腔静脉2例;脾动脉开口于肠系膜上动脉2例;胃左动脉开口于肠系膜上动脉1例;肝总动脉开口于腹主动脉1例;十二指肠前门静脉2例;合并先天性心脏病2例。结论CT不仅可清晰显示脾脏的数目及位置,而且可显示合并其他内脏异常及心血管畸形,对多脾综合征可做出准确、全面的诊断。
[Abstract]:Objective to investigate the MSCT findings of polysplenic syndrome and its diagnostic value. Methods the clinical and CT findings of 10 patients with polysplenic syndrome were retrospectively analyzed. Results the CT findings of 9 cases with multiple organ and cardiovascular system malformations were as follows: (1) multiple splenic nodules were found only in 1 case with atrial septal defect (ASD). The number of spleen was 4 ~ 14; (2) visceral abnormality. There were 1 case of total visceral inversion, 3 cases of partial visceral inversion, 6 cases of short pancreas, 1 case of annular pancreas, 2 cases of horizontal liver, 1 case of intestinal malrotation, 1 case of horseshoe kidney, 3 cases of isomerism on left side of both lungs. (3) Cardiovascular malformation. The hepatic segment of inferior vena cava was absent, the hepatic vein flowed directly into the right atrium, the azygos vein or half azygos vein dilated with the superior vena cava in 8 cases, the double superior vena cava in 2 cases, the splenic artery opening in the superior mesenteric artery in 2 cases; The left gastric artery opened to the superior mesenteric artery in 1 case, the common hepatic artery to the abdominal aorta in 1 case, the anterior portal vein to the duodenum in 2 cases, and congenital heart disease to 2 cases. Conclusion CT can not only clearly display the number and location of spleen, but also show other visceral abnormalities and cardiovascular malformations. Ct can make an accurate and comprehensive diagnosis of polysplenic syndrome.
【作者单位】：云南曲靖市第一人民医院放射科;解放军第425医院放射科;第三军医大学新桥医院放射科;
【分类号】：R551.1;R816

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