185例大前庭水管综合征患者的听力学特点分析

发布时间：2018-02-25 05:15

本文关键词： 大前庭水管综合征气骨导差短潜伏期负反应波　出处：《听力学及言语疾病杂志》2014年05期 　论文类型：期刊论文

【摘要】：目的探讨大前庭水管综合征(large vestibular aqueduct syndrome,LVAS)患者的听力学特点。方法对185例(370耳)LVAS患者进行纯音测听及声导抗、ABR、DPOAE、颞骨高分辨CT、头颅MRI检查,分析其特点。结果 183例(366耳)患者CT检查均提示双侧前庭水管扩大,2例(2耳)提示单侧前庭水管扩大;120例(240耳)行MRI检查,238耳均提示内淋巴囊扩大;112例(224耳)行纯音听阈测试,1例(1耳)听力正常,28例(55耳)为感音神经性聋,85例(168耳)呈混合性聋,其中152耳鼓室导抗图为A型的混合性聋患者,其低频气骨导差较大,中高频气骨导差较小;105例(210耳)行声导抗检测显示鼓室导抗图为A型192耳(其中低频引出声反射7耳),As型1耳,Ad型1耳,B型7耳,C型9耳;176例(352耳)行ABR检测,出现声诱发短潜伏期负反应波(acoustically evoked short latency negative response,ASNR)89例(124耳),占50.6%(89/176),ASNR平均波潜伏期在95dB SPL刺激声强时为3.04±0.29ms,在90dB SPL时为3.12±0.28ms;185例(370耳)DPOAE均未引出。结论 LVAS患者在中耳功能正常时其纯音听阈显示低频气骨导差较大、中高频气骨导差较小的混合性聋,ABR测试可引出特征性的ASNR。
[Abstract]:Objective to investigate the audiological characteristics of large vestibular aqueduct syndrome (LVASS) patients with large vestibular aqueduct syndrome. Methods 185 patients with large vestibular aqueduct syndrome were examined by pure tone audiometry, ABRV DPOAE, high resolution CTs of temporal bone and head MRI. Results CT examination of 183 patients with dilatation of vestibular aqueduct (2 patients with dilatation of vestibular aqueduct in 2 ears) and unilateral vestibular aqueduct dilatation in 120 patients with dilatation of vestibular aqueduct (n = 240). MRI examination showed enlargement of endolymphatic sac in 112 patients (n = 224). A pure tone hearing threshold test was performed in 1 case (n = 1) hearing normal (n = 28, n = 55) being sensorineural deafness (n = 85, n = 168)) mixed deafness. In 152 cases of mixed deafness with type A tympanic ventricular impedance, the low frequency air-bone conductance difference was larger. The acoustic impedance test showed that the tympanogram was A type in 192 ears (including 7 ears of low frequency evolutive acoustic reflex 7 ears of ad type 1 ear of ad type 1 ear of B type 7 ears of 7 ears of type C and 9 cases of 352 ears of type C). There were 89 cases of evoked short latency negative responseus ASNRV with acoustically evoked short latency, accounting for 50.6% 89 / 176% ASNRN, which was 3.04 卤0.29 msat 95 dB SPL stimulation intensity and 3.12 卤0.28 Ms DPOAE at 90 dB SPL. Conclusion in LVAS patients with normal middle ear function, the average latency is 3.04 卤0.29 ms. conclusion the median ear function of LVAS patients is normal. Its pure tone hearing threshold shows that the low frequency air-bone conductance difference is great. The ABR test of mixed deafness with low air-bone conductance in middle and high frequency can lead to characteristic ASNRs.
【作者单位】：安徽省立医院耳鼻咽喉头颈外科;
【分类号】：R764.43

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